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1 болезнь Дарье
1) Medicine: Darier's disease2) Genetics: Darier disease, keratosis follicularis -
2 болезнь Дарье
болезнь Дарье
фолликулярный дискератоз
НЗЧ кожи, проявляется обычно после полового созревания, характеризуется наличием кератиновых узелков (в основном на спине и голове), деформацией ногтей и др. симптомами; наследуется по аутосомно-доминантному типу, считается, что Б.Д. обусловлена мутациями в одном из генов цитоскелетных белков, вероятно, локализованном на хромосоме 1.
[Арефьев В.А., Лисовенко Л.А. Англо-русский толковый словарь генетических терминов 1995 407с.]Тематики
Синонимы
EN
Русско-английский словарь нормативно-технической терминологии > болезнь Дарье
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3 фолликулярный дискератоз
Darier's disease, morbus darier, keratosis follicularБольшой русско-английский медицинский словарь > фолликулярный дискератоз
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4 болезнь Дарье
Darier's disease, keratosis follicularisБольшой русско-английский медицинский словарь > болезнь Дарье
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5 саркоидоз
1) General subject: Boeck disease (увеличение лимфатических узлов, появление capкоидов на коже лица, сгибательных поверхностях конечностей, а на носу, щеках, веках, ушных раковинах, тыле и пальцах кистей - ознобленной волчанки кр)2) Medicine: Besnier-Boeck-Schaumann, Besnier-Boeck-Schaumann disease, Besnier-Boeck-Schaumann syndrome, Boeck's disease, Scaumann's disease, Schaumann's disease, sarcoidosis, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, Schaumann disease -
6 болезнь Бека
Medicine: Besnier-Boeck-Schaumann disease, Besnier-Boeck-Schaumann syndrome, Boeck's disease, sarcoidosis, Boeck disease (системное поражение мезенхимальной ткани и лимфатического аппарата с множественными клиническими проявлениями, в основе которого лежит образование воспалительной гранулемы), Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, Schaumann disease, Schaumann's disease -
7 доброкачественный гранулематоз
Medicine: Besnier-Boeck-Schaumann disease (лимфо), Besnier-Boeck-Schaumann syndrome (лимфо), Boeck's disease (лимфо), sarcoidosis (лимфо), Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > доброкачественный гранулематоз
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8 доброкачественный лимфогранулематоз
1) General subject: Schaumann's disease (увеличение лимфатических узлов, появление capкоидов на коже лица, сгибательных поверхностях конечностей, а на носу, щеках, веках, ушных раковинах, тыле и пальцах к)2) Medicine: Besnier-Boeck-Schaumann disease, Besnier-Boeck-Schaumann syndrome, Boeck's disease, sarcoidosis, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, Schaumann disease, Boeck diseaseУниверсальный русско-английский словарь > доброкачественный лимфогранулематоз
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9 ангиолюпоид
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's disease -
10 болезнь Меллера-Бека
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > болезнь Меллера-Бека
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11 болезнь Мортимера
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's disease -
12 гранулематоз Гатчинсона-Бека
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > гранулематоз Гатчинсона-Бека
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13 доброкачественный узловатый эпителиозноклеточный ретикулез
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > доброкачественный узловатый эпителиозноклеточный ретикулез
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14 лимфонодулярнолегочный саркоидоз
Medicine: Besnier-Boeck-Schaumann syndrome, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's disease, Boeck disease, Besnier-Boeck-Schaumann diseaseУниверсальный русско-английский словарь > лимфонодулярнолегочный саркоидоз
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15 люпоид Бека
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's disease -
16 люпоидный туберкулёз
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > люпоидный туберкулёз
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17 ознобленная волчанка
Medicine: lupus pernio, Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > ознобленная волчанка
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18 саркоид Бенье-Бека
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > саркоид Бенье-Бека
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19 саркоид Дарье-Русси
Medicine: miliary lupoid, Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's diseaseУниверсальный русско-английский словарь > саркоид Дарье-Русси
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20 саркоидоз Бека
Medicine: Besnier-Boeck-Schaumann syndrome, Besnier-Boeck-Schaumann disease, Boeck disease, Boeck sarcoid, Boeck's sarcoid, Schaumann syndrome, benign lymphogranulomatosis, benign lymphogranulomatosis of Schaumann, Besnier-Boeck disease, Boeck's sarcoidosis, Hutchinson-Boeck syndrome, Darier-Roussy sarcoid, lupus pernio of Besnier, miliary lupoid of Boeck, sarcoidoses, sarcoidosis, Schaumann disease, Schaumann's disease
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См. также в других словарях:
Darier disease — Darier disease. См. фолликулярный дискератоз. (Источник: «Англо русский толковый словарь генетических терминов». Арефьев В.А., Лисовенко Л.А., Москва: Изд во ВНИРО, 1995 г.) … Молекулярная биология и генетика. Толковый словарь.
Darier disease — Darier White disease a slowly progressive, autosomal dominant disorder of keratinization caused by mutation in the ATP2A2 gene (locus: 12q23 q24.1), which encodes a calcium transporting ATPase of the sarcoplasmic reticulum. It is characterized by … Medical dictionary
Darier disease sign — Da·rier disease, sign (dah re aґ) [Jean Ferdinand Darier, French dermatologist, 1856–1938] see under disease and sign … Medical dictionary
Darier's disease — Classification and external resources Linear Darier s disease ICD 10 Q82.8 … Wikipedia
Darier's disease — Da·rier s disease dar yāz , där n a genetically determined skin condition characterized by patches of keratotic papules called also keratosis follicularis Da·rier dȧr yā Jean Ferdinand (1856 1938) French dermatologist. Darier is known for… … Medical dictionary
Darier-White disease — Da·rier White disease (dah re aґ hwītґ) [J.F. Darier; James Clarke White, American dermatologist, 1833–1916] see under disease … Medical dictionary
Darier's disease — noun a rare hereditary condition marked by dark crusted patches (sometimes containing pus) • Syn: ↑keratosis follicularis • Hypernyms: ↑keratosis * * * där¦yāz, dȧ(r) noun Usage: usually capitalized 1st D Etymology: a … Useful english dictionary
Disease — Illness or sickness often characterized by typical patient problems (symptoms) and physical findings (signs). Disruption sequence: The events that occur when a fetus that is developing normally is subjected to a destructive agent such as the… … Medical dictionary
Darier — Jean F., French dermatologist, 1856–1938. See D. disease, D. sign … Medical dictionary
Ferdinand-Jean Darier — Born 26 April 1856(1856 04 26) Budapest, Hungary Died 1938 (aged 81–82) Paris, France[citation needed] … Wikipedia
Wilson's disease — Classification and external resources A Kayser Fleischer ring (the brown ring on the edge of the iris) is common in Wilson s disease, especially when neurological symptoms are present ICD … Wikipedia